New guideline for treating Allan-Herndon-Dudley syndrome

· Medical Xpress

by Ruhr University Bochum

edited by Lisa Lock, reviewed by Andrew Zinin

Lisa Lock

Scientific Editor

Meet our editorial team
Behind our editorial process

Andrew Zinin

Chief Editor

Meet our editorial team
Behind our editorial process Editors' notes

This article has been reviewed according to Science X's editorial process and policies. Editors have highlighted the following attributes while ensuring the content's credibility:

fact-checked

trusted source

proofread

The GIST Add as preferred source


An overview of the guidelines for caring for those affected. Credit: Johannes W. Dietrich

Allan-Herndon-Dudley syndrome is a rare congenital disease of thyroid metabolism. It occurs in approximately 1 out of every 70,000 male newborns, and its effects are devastating. Since early 2025, a medication has been approved in Europe that can alleviate symptoms and extend patients' life expectancy. However, the dosage is complicated.

A team of specialists working with Professor Johannes W. Dietrich from the Department of Diabetology, Endocrinology and Metabolism at the Ruhr University Bochum St. Josef Hospital, Germany—and director of the Center for Rare Endocrine Diseases at the Center for Rare Diseases Ruhr (CeSER)—has published a guideline for treating the disease in the journal Hormone Research in Paediatrics.

Severe symptoms and short life expectancy

In Allan-Herndon-Dudley syndrome, a mutation in the MCT8 protein severely disrupts the transport of thyroid hormones into and out of certain cell types. The disease is inherited through the X chromosome, is very rare and has devastating consequences for people afflicted by it: severe developmental disorders with consequent major intellectual disability, muscle weakness and cardiac arrhythmias are typical.

"Patients usually never learn how to speak or walk, and, due to an elevated concentration of the thyroid hormone T3, they usually die prematurely from cardiovascular complications," says Dietrich. "The average life expectancy is 35 years."

Individual treatment plan

A newly approved medication, the nonclassical thyroid hormone TRIAC, is now available in Europe. This therapy can alleviate some of the symptoms and extend patients' life expectancy, although the dosage is highly complex.

A working group from Germany and Switzerland developed the new guideline based on extensive research of the literature and its own clinical experience in pediatric neurology and endocrinology. It provides recommendations for a comprehensive, multidisciplinary treatment strategy for patients in all age groups while also considering monitoring of the most important systems and secondary diseases.

"Because the symptoms and long-term courses associated with this disease can vary widely, individual treatment plans for the patients are necessary," says Dietrich.

More information

Johannes W. Dietrich et al, Clinical and Biochemical Monitoring of Monocarboxylate Transporter 8 Deficiency (Allan-Herndon-Dudley Syndrome) across the Lifespan: Practical Considerations for Multidisciplinary Care, Hormone Research in Paediatrics (2026). DOI: 10.1159/000551857

Key medical concepts

Arrhythmia

Clinical categories

EndocrinologyPediatricsNeurologyChildren's health Provided by Ruhr University Bochum Who's behind this story?

Lisa Lock

BA art history, MA material culture. Former museum editor, paramedic, and transplant coordinator. Editing for Science X since 2021. Full profile →

Andrew Zinin

Master's in physics with research experience. Long-time science news enthusiast. Plays key role in Science X's editorial success. Full profile →

Citation: New guideline for treating Allan-Herndon-Dudley syndrome (2026, July 8) retrieved 9 July 2026 from https://medicalxpress.com/news/2026-07-guideline-allan-herndon-dudley-syndrome.html This document is subject to copyright. Apart from any fair dealing for the purpose of private study or research, no part may be reproduced without the written permission. The content is provided for information purposes only.